Abstract

Background: Sturge Weber syndrome (SWS) is a rare neurocutaneous

disease characterized with a port-wine stain and ipsilateral leptomeningeal

angiomas. It may cause wide variety of neurological signs and symptoms.

Case: A 63-year-old female patient with a port-wine stain on her face was

followed up in our department with two different clinical presentation in

which symptoms of transient ischemic attack and focal epileptic seizures in

two years intervals. The investigation of the cause of the transient ischemic

attacks showed dissection of the right cavernous internal carotid artery.

Conclusion: To the best of our knowledge, this is the first case in the

literature, such an advanced ages as in our case, central nervous system

involvement could be related by congenital abnormalities of the vascular

bed.