Abstract

One year old patient was referred to our clinic with the diagnosis of total anomalous venous connection. Despite tachycardia and pulmonary plethora, the patient was acyanotic and the transthoracic echocardiography detected pulmonary venous baffle or vertical vein. Considering these doubtful findings, computed tomography angiography was performed and revealed that right pulmonary veins was draining towards an enlarged vena cava superior while right pulmonary veins into the left atrium. Furthermore, a fibrotic tissue that encurtains the mitral orifice was observed. Consequently, the patient underwent surgery with the diagnoses of cor triatriatum sinistrum and partial anomalous pulmonary connection. The exact diagnosis was confirmed after a profound surgical inspection; afterwards, then the whole process was accomplished smoothly and the patient discharged in good condition.