Abstract

Distal renal tubular acidosis (dRTA) resul ts from ineffective addition of hydrogen ions into the lumen of the distal nephron. The syndrome is manifested by hyperchloremic metabolic acidosis often associated with hypokalemia. Also, hypercalcemia and nephrocalcinosis are usually unexpected in infaney. We deseribe a 19- day- old full-term boy presented with poor feeding and inactivation. Laboratory investigation revealed hypercalcemia (12.9 mg/dl) and nephrocalcinosis secondary to distal renal tubular acidosis. In conclusion, dRTA should be included in the differential diagnosis of hypercalcemia that may accelerate the development of nephrocalcinosis in the neonate.